Right ventricular involvement in left ventricular non-compaction cardiomyopathy

Cardiol J. 2022;29(3):454-462. doi: 10.5603/CJ.a2020.0095. Epub 2020 Jul 10.

Abstract

Background: Left ventricular non-compaction cardiomyopathy (LVNC) features extensive trabeculations. Involvement of the right ventricle (RV) has been reported; however, distinction from normal RV trabeculation is difficult. This study aimed at assessing RV morphology and function in LVNC by cardiac magnetic resonance (CMR) and transthoracic echocardiography (TTE).

Methods: Dimensional and functional parameters were assessed according to guidelines. Novel CMR parameters were RV end-diastolic (ED) trabeculated area, RV ED trabeculated volume, and RV ED non-compacted to compacted (NC/N) ratio in short axis (SAX) as well as in four-chamber view (4CH).

Results: Twenty patients with LVNC and 20 controls were included. RV size and function were comparable in LVNC and controls and exhibited a good correlation between TTE and CMR. Although RV trabeculated area, RV trabeculated volume, and RV ED NC/C ratio in SAX as well as in 4CH were larger in LVNC, there was a major overlap with values in controls. RV ED NC/C ratio in SAX correlated with LV ED NC/C ratio (not in 4CH). Quantitative assessment of RV non-compaction was not feasible in TTE.

Conclusions: Right ventricle size and function in LVNC can be measured by CMR and TTE, while RV trabeculation can only be quantified by CMR. RV myocardium displays more trabeculations in LVNC; however, overlap with normal individuals is extensive, not allowing separation of patients with LVNC from controls.

Keywords: cardiac magnetic resonance imaging; echocardiography; left ventricular non-compaction cardiomyopathy; trabeculation.

MeSH terms

  • Cardiomyopathies*
  • Heart Ventricles
  • Humans
  • Isolated Noncompaction of the Ventricular Myocardium* / diagnosis
  • Isolated Noncompaction of the Ventricular Myocardium* / diagnostic imaging
  • Magnetic Resonance Imaging, Cine / methods
  • Predictive Value of Tests

Grants and funding

The study was supported by the Swiss Heart Foundation.