[Mild encephalitis/encephalopathy with a reversible splenial lesion (MERS) with a family history: an adult case]

Rinsho Shinkeigaku. 2022 Mar 29;62(3):224-230. doi: 10.5692/clinicalneurol.cn-001697. Epub 2022 Mar 25.
[Article in Japanese]

Abstract

We present an adult case of mild encephalitis/encephalopathy with a reversible splenial lesion (MERS). A 26-year-old man with a family history of MERS presented to our hospital owing to dysarthria and dysesthesia of the right side of his body. The duration of these symptoms was approximately 4 hours. T2 and diffusion weighted MRI showed high signal intensity lesions in the bilateral deep white matter. On a 3-week follow-up MRI, the lesions had completely disappeared. We attributed this clinical course and image findings to MERS. The patient had experienced similar symptoms at the age of 8 years old. Furthermore, his younger brother showed a similar clinical history and experienced a few recurrence events during the age of 9-16 years old. The mechanism of MERS remains controversial. However, similar to our case, there are some case reports with a family history. In addition, a previous report has confirmed the existence of a heterozygous variant in the myelin regulatory factor gene in patients with MERS. Some genetic factors may induce MERS, especially with extensive white matter lesions.

Keywords: deep white matter lesion; familial; mild encephalitis/encephalopathy with a reversible splenial lesion (MERS); transient ischemic attack; type 2 lesion.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Brain Diseases* / diagnosis
  • Child
  • Corpus Callosum / diagnostic imaging
  • Corpus Callosum / pathology
  • Diffusion Magnetic Resonance Imaging
  • Encephalitis* / diagnosis
  • Encephalitis* / etiology
  • Humans
  • Magnetic Resonance Imaging
  • Male