Background: The presence of a rare lesion for pediatric population, encountered in twins, as far as we know, is an exceptional event. The event made the management of a pathology, for which there are no guidelines in the pediatric field, even more delicate.
Case report: Two twin sisters came to our attention, a short time after each other, due to the presence of a voluminous abdominal mass. After complete resection, the histological diagnosis was that of a paraovarian cystoadenofibroma.
Discussion: In pediatric surgery being minimally invasive is mandatory. However in selected cases the only objective, especially speaking of pediatric patients, ais to be radical and to protect the adnexal structures.
Keywords: Paraovarian cystoadenofibroma; ovary; pediatric surgery; twins; urogenital system; 儿科手术; 卵巢; 卵巢冠囊腺纤维瘤; 双胞胎; 泌尿生殖系统.