First Report of Thoracic Carcinoma With DEK::AFF2 Rearrangement: A Case Report

J Thorac Oncol. 2022 Aug;17(8):1050-1053. doi: 10.1016/j.jtho.2022.05.009. Epub 2022 Jun 28.

Abstract

DEK::AFF2 carcinomas of the head and neck region have been recently described and reported to have aggressive clinical behavior but exceptional sensitivity to immunotherapy. We report a case of a 26-year-old female, never smoker, with a 5.2-cm left lower lobe central lung mass, with morphologic features identical to those reported for DEK::AFF2 head and neck carcinomas, including mixed papillary exophytic and invasive components, squamous/basaloid features, and monomorphic cytomorphology. DEK (exon 7)::AFF2 (exon 9) fusion was identified by whole-transcriptome RNA sequencing. This is the first report of thoracic DEK::AFF2 carcinoma, indicating that these tumors are not confined to the head and neck region but can involve both upper and lower respiratory tracts. This entity should be considered in the differential diagnosis of squamous cell carcinomas in never smokers lacking other known oncogenic mutations.

Keywords: AFF2; Carcinoma; Case report; DEK; Lung.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Research Support, N.I.H., Extramural

MeSH terms

  • Adult
  • Carcinoma, Squamous Cell* / genetics
  • Carcinoma, Squamous Cell* / pathology
  • Chromosomal Proteins, Non-Histone / genetics
  • Chromosomal Proteins, Non-Histone / metabolism
  • Female
  • Gene Fusion
  • Head and Neck Neoplasms*
  • Humans
  • Lung Neoplasms* / genetics
  • Nuclear Proteins / genetics
  • Oncogene Proteins / genetics
  • Oncogene Proteins / metabolism
  • Poly-ADP-Ribose Binding Proteins / genetics
  • Thoracic Neoplasms* / genetics

Substances

  • AFF2 protein, human
  • Chromosomal Proteins, Non-Histone
  • DEK protein, human
  • Nuclear Proteins
  • Oncogene Proteins
  • Poly-ADP-Ribose Binding Proteins