Syndromic Synostosis: Frontofacial Surgery

Kevin Chen; Katelyn Kondra; Eric Nagengast; Jeffrey A Hammoudeh; Mark M Urata

doi:10.1016/j.coms.2022.03.001

Syndromic Synostosis: Frontofacial Surgery

Oral Maxillofac Surg Clin North Am. 2022 Aug;34(3):459-466. doi: 10.1016/j.coms.2022.03.001. Epub 2022 Jun 30.

Authors

Kevin Chen¹, Katelyn Kondra¹, Eric Nagengast², Jeffrey A Hammoudeh³, Mark M Urata⁴

Affiliations

¹ Division of Plastic and Maxillofacial Surgery, Children's Hospital Los Angeles, 4650 West Sunset Boulevard, Mailstop 96, Los Angeles, CA 90027, USA.
² Division of Plastic and Reconstructive Surgery, Keck Medicine of USC, 1520 San Pablo Street, Los Angeles, CA 90033, USA.
³ Division of Plastic and Maxillofacial Surgery, Children's Hospital Los Angeles, 4650 West Sunset Boulevard, Mailstop 96, Los Angeles, CA 90027, USA; Division of Plastic and Reconstructive Surgery, Keck Medicine of USC, 1520 San Pablo Street, Los Angeles, CA 90033, USA; Herman Ostrow School of Dentistry, University of Southern California, 925 West 34th Street, Los Angeles, CA 90089, USA; Division of Oral and Maxillofacial Surgery, University of Southern California, 925 West 34th Street, Los Angeles, CA 90089, USA. Electronic address: jhammoudeh@chla.usc.edu.
⁴ Division of Plastic and Maxillofacial Surgery, Children's Hospital Los Angeles, 4650 West Sunset Boulevard, Mailstop 96, Los Angeles, CA 90027, USA; Division of Plastic and Reconstructive Surgery, Keck Medicine of USC, 1520 San Pablo Street, Los Angeles, CA 90033, USA; Herman Ostrow School of Dentistry, University of Southern California, 925 West 34th Street, Los Angeles, CA 90089, USA; Division of Oral and Maxillofacial Surgery, University of Southern California, 925 West 34th Street, Los Angeles, CA 90089, USA.

PMID: 35786530
DOI: 10.1016/j.coms.2022.03.001

Abstract

Frontofacial surgery, encompassing the monobloc with or without facial bipartition and the box osteotomy, can treat the frontal bone and midface simultaneously, providing comprehensive improvement in facial balance. Complex pediatric patients with genetic syndromes and craniosynostosis are most optimized by an interdisciplinary team of surgeons, pediatricians, geneticists, speech pathologists, audiologists, dietitians, pediatric dentists, orthodontists, and psychosocial support staff to manage the myriad of challenges and complications throughout early childhood and beyond. Despite early treatment of the anterior and posterior cranial vault, these patients frequently have resultant frontal and/or midface hypoplasia and orbital abnormalities that are best managed with simultaneous surgical treatment.

Keywords: Facial bipartition; Frontofacial surgery; Monobloc; Orbital box osteotomies; Syndromic craniosynostosis.

Publication types

Review

MeSH terms

Child
Child, Preschool
Craniosynostoses* / surgery
Frontal Bone / surgery
Humans
Osteogenesis, Distraction*
Osteotomy