IPF Respiratory Symptoms Management - Current Evidence

Piotr Janowiak; Amelia Szymanowska-Narloch; Alicja Siemińska

doi:10.3389/fmed.2022.917973

IPF Respiratory Symptoms Management - Current Evidence

Front Med (Lausanne). 2022 Jul 28:9:917973. doi: 10.3389/fmed.2022.917973. eCollection 2022.

Authors

Piotr Janowiak¹, Amelia Szymanowska-Narloch¹, Alicja Siemińska¹

Affiliation

¹ Department of Pulmonology, Medical University of Gdańsk, Gdańsk, Poland.

Abstract

Idiopathic pulmonary fibrosis (IPF) is a progressive, chronic disease of the lungs which is characterized by heavy symptom burden, especially in the last year of life. Despite recently established anti-fibrotic treatment IPF prognosis is one of the worst among interstitial lung diseases. In this review available evidence regarding pharmacological and non-pharmacological management of the main IPF symptoms, dyspnea and cough, is presented.

Keywords: ambulatory oxygen therapy (AOT); breathlessness; cough; dyspnea; high flow nasal cannula (HFNC); idiopathic pulmonary fibrosis (IPF); non-invasive positive pressure ventilation (NIPPV); non-invasive ventilation (NIV).

Publication types

Review