Locus coeruleus degeneration and cerebellar gray matter changes in essential tremor

J Neurol. 2023 Feb;270(2):780-787. doi: 10.1007/s00415-022-11409-z. Epub 2022 Oct 4.

Abstract

Background: The pathophysiology of essential tremor (ET) is not fully understood, and studies suggest pathological changes mainly occur in the cerebellum and locus coeruleus (LC).

Methods: Fifty-three ET patients, including 30 patients with head tremor (h-ET), 23 patients without head tremor (nh-ET), 71 age and education matched healthy controls (HCs) were enrolled. All participants underwent Neuromelanin-sensitive magnetic resonance imaging (NM-MRI) and T1 scans on a 3-Tesla MR system. Next, we assessed the relationship between the contrast-to-noise ratio of LC (CNRLC) and the score of The Essential Tremor Rating Assessment Scale (TETRAS) and cerebellum gray matter (GM) volume.

Results: Significant difference of CNRLC was found between ET and HC groups. The CNRLC of ET groups is lower than the HC group (p = 0.031). Subgroup analysis showed that the CNRLC in nh-ET was significantly lower than HCs (p = 0.016). Compared to HCs, h-ETs showed marked atrophy in the cerebellum: the vermis IV-V and lobule VI (GRF corrected, p < 0.05). A significant negative correlation was found between CNRLC and the vermis lobule IV-V in h-ETs (r = - 0.651, p < 0.001). No significant correlation was found between CNRLC and TETRAS scores.

Conclusion: The LC and the cerebellum might both involve in the pathophysiology of ET. LC evaluation using NM-MRI might be an effective tool for us to explore the pathophysiology of ET further.

Keywords: Cerebellum; Essential tremor; Locus coeruleus; Magnetic resonance imaging.

MeSH terms

  • Cerebellum / diagnostic imaging
  • Cerebellum / pathology
  • Essential Tremor* / diagnostic imaging
  • Essential Tremor* / pathology
  • Gray Matter* / diagnostic imaging
  • Gray Matter* / pathology
  • Humans
  • Locus Coeruleus / diagnostic imaging
  • Locus Coeruleus / pathology
  • Magnetic Resonance Imaging / methods
  • Tremor / pathology