ANCA-negative pauci-immune crescentic glomerulonephritis associated with Fabry disease: lesson for the clinical nephrologist

J Nephrol. 2023 Apr;36(3):635-638. doi: 10.1007/s40620-022-01533-4. Epub 2023 Feb 16.

Charles Ronsin^{1

2}, Lola Jacquemont³, Angelo Testa⁴, Karine Renaudin⁵, Simon Ville^{3

6}

¹ Department of Nephrology and Immunology, Nantes University Hospital, Nantes, France. charles.ronsin@chu-nantes.fr.
² Nephrology and Transplantation Department, University of Nantes, 30 bd Jean Monnet, 44093, Nantes Cedex 01, France. charles.ronsin@chu-nantes.fr.
³ Department of Nephrology and Immunology, Nantes University Hospital, Nantes, France.
⁴ E.C.H.O, Site Confluent-Rezé, Rezé, France.
⁵ Department of Pathology, Nantes University Hospital, Nantes, France.
⁶ Centre de Recherche en Transplantation et Immunologie, UMR 1064, INSERM, Université de Nantes, Nantes, France.

No abstract available

Keywords: ANCA-negative vasculitis; Fabry disease; Kidney pathology; Pauci-immune crescentic glomerulonephritis.

MeSH terms