A Case of Primary Intraosseous Adenoid Cystic Carcinoma of the Mandible

Erika Sasaki; Kenji Yamagata; Takayuki Hagiwara; Ryo Takasaki; Satoshi Fukuzawa; Fumihiko Uchida; Naomi Ishibashi-Kanno; Hiroki Bukawa

doi:10.1155/2023/2422086

A Case of Primary Intraosseous Adenoid Cystic Carcinoma of the Mandible

Case Rep Dent. 2023 May 23:2023:2422086. doi: 10.1155/2023/2422086. eCollection 2023.

Authors

Erika Sasaki¹, Kenji Yamagata¹, Takayuki Hagiwara¹, Ryo Takasaki¹, Satoshi Fukuzawa¹, Fumihiko Uchida¹, Naomi Ishibashi-Kanno¹, Hiroki Bukawa¹

Affiliation

¹ Department of Oral and Maxillofacial Surgery, Institute of Clinical Medicine, Faculty of Medicine, University of Tsukuba, Tsukuba, Ibaraki 305-8575, Japan.

Abstract

Primary intraosseous adenoid cystic carcinoma (PIACC) of the jaw is rare. To our knowledge, only 51 cases have been reported in the English literature. We present a rare case of PIACC arising in the mandible with multiple bone metastases and review the previous articles. A 70-year-old woman presented with paresthesia of the right chin and lower gingiva for 4 months. Radiography revealed an irregular radiolucent region on the right side of the ramus, infiltrating to the mandibular canal. Biopsy revealed a pathological diagnosis of adenoid cystic carcinoma. Multiple bone metastases were present in the sternum, scapula, and thighs. The treatment effect was progressive disease for chemotherapy; therefore, best supportive care was provided for 3 years.

Publication types

Case Reports