Case report: Beneficial long-term effect of the atrial-flow-regulator device in a pediatric patient with idiopathic pulmonary arterial hypertension and recurring syncope

Joseph Pattathu; Sebastian Michel; Anja Ingrid Tengler; Guido Mandilaras; Andre Jakob; Robert Dalla Pozza; Nikolaus A Haas

doi:10.3389/fcvm.2023.1197985

Case report: Beneficial long-term effect of the atrial-flow-regulator device in a pediatric patient with idiopathic pulmonary arterial hypertension and recurring syncope

Front Cardiovasc Med. 2023 Sep 8:10:1197985. doi: 10.3389/fcvm.2023.1197985. eCollection 2023.

Authors

Joseph Pattathu^#¹, Sebastian Michel^#¹, Anja Ingrid Tengler¹, Guido Mandilaras¹, Andre Jakob¹, Robert Dalla Pozza¹, Nikolaus A Haas¹

Affiliation

¹ Division of Pediatric Cardiology and Intensive care, University Hospital, Ludwigs-Maximilians University Munich, Munich, Germany.

^# Contributed equally.

Abstract

We report the long-term effect after successfully implanting an 8 mm Atrial-flow-regulator (AFR) device in a 7-year-old girl with idiopathic pulmonary hypertension with persistent syncope under triple therapy with significant improvement after implantation and absence of any further syncope. Early Implantation of the AFR device (Occlutech, Germany) can be efficient and safe interventional therapy option for pulmonary arterial hypertension with a history of syncope.

Keywords: atrial flow regulator (AFR) - device; atrial septostomy; cardiac catherization intervention; pediatric cardiology; pulmonary arterial hypertension.

Publication types

Case Reports