Subependymomas of the fourth ventricle: To operate or not to operate?

J Clin Neurosci. 2023 Dec:118:147-152. doi: 10.1016/j.jocn.2023.10.025. Epub 2023 Nov 7.

Abstract

Background: There is a paucity of literature regarding the clinical characteristics and management of subependymomas of the fourth ventricle due to their rarity. Here, we describe the operative and non-operative management and outcomes of patients with such tumors.

Methods: This retrospective single-institution case series was gathered after Institutional Review Board (IRB) approval. Patients diagnosed with a subependymoma of the fourth ventricle between 1993 and 2021 were identified. Clinical, radiology and pathology reports along with magnetic resonance imaging (MRI) images were reviewed.

Results: Patients identified (n = 20), showed a male predominance (n = 14). They underwent surgery (n = 9) with resection and histopathological confirmation of subependymoma or were followed with imaging surveillance (n = 11). The median age at diagnosis was 51.5 years. Median tumor volume for the operative cohort was 8.64 cm3 and median length of follow-up was 65.8 months. Median tumor volume for the non-operative cohort was 0.96 cm3 and median length of follow-up was 78 months. No tumor recurrence post-resection was noted in the operative group, and no tumor growth from baseline was noted in the non-operative group. Most patients (89 %) in the operative group had symptoms at diagnosis, all of which improved post-resection. No patients were symptomatic in the non-operative group.

Conclusions: Surgical resection is safe and is associated with alleviation of presenting symptoms in patients with large tumors. Observation and routine surveillance are warranted for smaller, asymptomatic tumors.

Keywords: Intraventricular; Neuroimaging; Subependymoma; Surgery.

MeSH terms

  • Cerebral Ventricle Neoplasms* / diagnostic imaging
  • Cerebral Ventricle Neoplasms* / surgery
  • Female
  • Fourth Ventricle / diagnostic imaging
  • Fourth Ventricle / pathology
  • Fourth Ventricle / surgery
  • Glioma, Subependymal* / diagnostic imaging
  • Glioma, Subependymal* / surgery
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Neoplasm Recurrence, Local
  • Retrospective Studies