Nodular-Type Lichen Myxedematosus: A Rare Variant With Exclusive Involvement of the Hands-Report of Two Cases With a Comprehensive Review of the Literature

Am J Dermatopathol. 2024 Jan 1;46(1):36-39. doi: 10.1097/DAD.0000000000002589.

Abstract

Lichen myxedematosus (LM) is an uncommon cutaneous mucinosis characterized by the deposition of mucin and fibroblast proliferation in the dermis. This condition can be classified into 2 forms: a diffuse/generalized LM, also known as scleromyxedema, associated with monoclonal gammopathy and systemic implications, and a localized form, primarily affecting the skin. Within the localized form, nodular-type LM is a rare variant presenting as firm, skin-colored to pinkish mucinous nodules. In this article, we report 2 new cases of nodular-type LM with exclusive involvement of the hands and provide a comprehensive review of the diagnosis, histopathological aspects, and therapeutic considerations of this rare condition.

Publication types

  • Review
  • Case Reports

MeSH terms

  • Hand / pathology
  • Humans
  • Scleromyxedema* / diagnosis
  • Scleromyxedema* / pathology
  • Skin / pathology
  • Skin Diseases* / pathology
  • Upper Extremity / pathology