[Intracranial phosphaturic mesenchymal tumor: report of a case]

Y Han; S J Cheng; X Su; F Yang

doi:10.3760/cma.j.cn112151-20230727-00031

[Intracranial phosphaturic mesenchymal tumor: report of a case]

Zhonghua Bing Li Xue Za Zhi. 2023 Dec 8;52(12):1293-1296. doi: 10.3760/cma.j.cn112151-20230727-00031.

[Article in Chinese]

Authors

Y Han¹, S J Cheng¹, X Su¹, F Yang¹

Affiliation

¹ Cancer Prevention and Treatment Institute of Chengdu, Department of Pathology, Chengdu Fifth People's Hospital (the Second Clinical Medical College, Affiliated Fifth People's Hospital of Chengdu University of Traditional Chinese Medicine), Chengdu 611137, China.

PMID: 38058054
DOI: 10.3760/cma.j.cn112151-20230727-00031

Abstract

磷酸盐尿性间叶性肿瘤是一种罕见的间叶性肿瘤，患者常伴有肿瘤相关性骨软化症，严重者可致残疾，绝大部分患者肿瘤完整切除后可治愈。该病镜下组织形态多样，可与多种间叶性肿瘤重叠，极易误诊。本文报道1例罕见的原发于颅内的磷酸盐尿性间叶性肿瘤，患者伴有低磷血症及骨软化症，镜下主要由温和的短梭形及卵圆形细胞组成，间质内见大量增生的毛细血管及散在厚壁血管，可见散在成熟脂肪细胞小灶。本例经过充分取材，并未发现特征性絮状钙化及破骨样巨细胞。.

Publication types

Case Reports

MeSH terms

Humans
Mesenchymoma* / surgery
Osteomalacia*
Soft Tissue Neoplasms*