Childhood Vasculitis

Indian J Pediatr. 2024 Oct;91(10):1056-1064. doi: 10.1007/s12098-023-04958-2. Epub 2023 Dec 15.

Abstract

Of the primary vasculitis pediatricians are familiar with, Kawasaki disease and IgA vasculitis are the most common. The other large, medium and small vessel vasculitis are seldom seen in practice. Though rare, early diagnosis and appropriate management is critical for the best outcome. Primary vasculitis in the pediatric age group have several differential diagnoses which range from infections to monogenic causes such as deficiency of Adenosine Deaminase -2. Each child, therefore, needs a careful systematic approach.

Keywords: Childhood vasculitis; Clinical approach to vasculitis in children; IgA vasculitis; Kawasaki disease.

Publication types

  • Review

MeSH terms

  • Adenosine Deaminase / deficiency
  • Adenosine Deaminase / genetics
  • Child
  • Diagnosis, Differential
  • Humans
  • Mucocutaneous Lymph Node Syndrome* / diagnosis
  • Vasculitis* / diagnosis

Substances

  • Adenosine Deaminase