The Spectrum of Dysregulated Aldosterone Production: An International Human Physiology Study

J Clin Endocrinol Metab. 2024 Aug 13;109(9):2220-2232. doi: 10.1210/clinem/dgae145.

Abstract

Context: Primary aldosteronism is a form of low-renin hypertension characterized by dysregulated aldosterone production.

Objective: To investigate the contributions of renin-independent aldosteronism and ACTH-mediated aldosteronism in individuals with a low-renin phenotype representing the entire continuum of blood pressure.

Design/participants: Human physiology study of 348 participants with a low-renin phenotype with severe and/or resistant hypertension, hypertension with hypokalemia, elevated blood pressure and stage I/II hypertension, and normal blood pressure.

Setting: 4 international centers.

Interventions/main outcome measures: The saline suppression test (SST) to quantify the magnitude of renin-independent aldosteronism; dexamethasone suppression and ACTH-stimulation tests to quantify the magnitude of ACTH-mediated aldosteronism; adrenal venous sampling to determine lateralization.

Results: There was a continuum of nonsuppressible and renin-independent aldosterone production following SST that paralleled the magnitude of the blood pressure continuum and transcended conventional diagnostic thresholds. In parallel, there was a full continuum of ACTH-mediated aldosteronism wherein post-SST aldosterone levels were strongly correlated with ACTH-stimulated aldosterone production (r = 0.75, P < .0001) and nonsuppressible aldosterone production postdexamethasone (r = 0.40, P < .0001). Beyond participants who met the criteria for primary aldosteronism (post-SST aldosterone of ≥10 ng/dL or ≥277 pmol/L), the continuum of nonsuppressible and renin-independent aldosterone production persisted below this diagnostic threshold, wherein 15% still had lateralizing aldosteronism amenable to surgical adrenalectomy and the remainder were treated with mineralocorticoid receptor antagonists.

Conclusion: In the context of a low-renin phenotype, there is a continuum of primary aldosteronism and dysregulated aldosterone production that is prominently influenced by ACTH. A large proportion of individuals with low renin may benefit from aldosterone-directed therapy.

Keywords: ACTH; aldosterone; hypertension; low-renin hypertension; primary aldosteronism.

Publication types

  • Multicenter Study

MeSH terms

  • Adrenal Glands / metabolism
  • Adrenocorticotropic Hormone* / blood
  • Adrenocorticotropic Hormone* / metabolism
  • Adult
  • Aged
  • Aldosterone* / blood
  • Aldosterone* / metabolism
  • Blood Pressure / physiology
  • Dexamethasone
  • Female
  • Humans
  • Hyperaldosteronism* / metabolism
  • Hypertension* / etiology
  • Hypertension* / metabolism
  • Male
  • Middle Aged
  • Renin* / blood

Substances

  • Aldosterone
  • Renin
  • Adrenocorticotropic Hormone
  • Dexamethasone