Phaeochromocytoma and paraganglioma

J Clin Pathol. 2024 Jul 18;77(8):507-516. doi: 10.1136/jcp-2023-209234.

Abstract

Phaeochromocytomas and paragangliomas are rare catecholamine-producing neuroendocrine tumours which can potentially cause catastrophic crises with high morbidity and mortality. This best practice article considers the causes and presentation of such tumours, screening and diagnostic tests, management of these patients and consideration of family members at risk.

Keywords: Adrenal Glands; CATECHOLAMINES; Endocrine System Diseases; Neuroendocrine Tumors.

Publication types

  • Review

MeSH terms

  • Adrenal Gland Neoplasms* / diagnosis
  • Adrenal Gland Neoplasms* / pathology
  • Adrenal Gland Neoplasms* / therapy
  • Catecholamines / metabolism
  • Humans
  • Paraganglioma* / diagnosis
  • Paraganglioma* / pathology
  • Pheochromocytoma* / diagnosis
  • Pheochromocytoma* / pathology

Substances

  • Catecholamines