How I do it: operative nuances of the Encephalo-Duro-Mio-Synangiosis (EDMS) technique for pediatric moyamoya disease and syndrome

Acta Neurochir (Wien). 2024 Jun 4;166(1):249. doi: 10.1007/s00701-024-06148-1.

Abstract

Background: Moyamoya disease, a progressive occlusive arteriopathy mainly affecting the supraclinoid internal carotid artery, leads to abnormal "Moyamoya vessels" and ischemic events in children due to decreased cerebral blood flow. Surgery, especially indirect revascularization, is suggested for pediatric Moyamoya cases.

Method: We present the Encephalo-Duro-Mio-Synangiosis (EDMS) technique, illustrated with figures and videos, based on 14 years' experience performing 71 surgeries by the senior author (SGJ) and the Moyamoya Interdisciplinary Workteam at "Prof. Dr. J. P. Garrahan" Pediatric Hospital.

Conclusion: EDMS is a simple and effective treatment for Moyamoya disease, enhancing procedure precision and safety, reducing associated risks, complications, and improving clinical outcomes.

Keywords: Cerebral arterial diseases; Encephalo-duro-mio-synangiosis; Indirect revascularization techniques; Moyamoya disease; Pediatric neurosurgery.

MeSH terms

  • Adolescent
  • Carotid Artery, Internal / diagnostic imaging
  • Carotid Artery, Internal / surgery
  • Cerebral Angiography / methods
  • Cerebral Revascularization* / methods
  • Child
  • Female
  • Humans
  • Male
  • Moyamoya Disease* / diagnostic imaging
  • Moyamoya Disease* / surgery
  • Treatment Outcome