Constitutional mismatch repair deficiency: a case on a commonly misinterpreted mutation in colon cancer

Clin J Gastroenterol. 2024 Oct;17(5):866-870. doi: 10.1007/s12328-024-02015-9. Epub 2024 Aug 2.

Abstract

It is estimated that 153,020 cases of CRC per year, with an increase in diagnoses in younger patients. We present a case of a female with an early presentation of Lynch Syndrome and CRC, who, on her third malignant presentation, was re-diagnosed as a constitutional mismatch repair deficiency.

Keywords: Colorectal cancer; HNPCC; Lynch syndrome; Mismatch repair.

Publication types

  • Case Reports

MeSH terms

  • Brain Neoplasms
  • Colonic Neoplasms / genetics
  • Colorectal Neoplasms / genetics
  • Colorectal Neoplasms, Hereditary Nonpolyposis* / diagnosis
  • Colorectal Neoplasms, Hereditary Nonpolyposis* / genetics
  • DNA Mismatch Repair / genetics
  • Diagnostic Errors
  • Female
  • Humans
  • Middle Aged
  • MutL Protein Homolog 1 / deficiency
  • MutL Protein Homolog 1 / genetics
  • Mutation
  • Neoplastic Syndromes, Hereditary / genetics

Substances

  • MutL Protein Homolog 1

Supplementary concepts

  • Turcot syndrome