Dermatofibrosarcoma protuberans

Int J Dermatol. 1984 Jul-Aug;23(6):396-401. doi: 10.1111/j.1365-4362.1984.tb03200.x.

Abstract

In view of the important clinicopathologic, evolutional, and ultrastructural characteristics of dermatofibrosarcoma Protuberans, a review was made of 30 patients seen during the last 25 years in Colombia's Instituto Nacional de Cancerologia. The incidence is low, accounting for 0.06% of all malignant tumors and 1.17% of all soft-parts sarcomas. The series comprises 19 women and 11 men, with the highest incidence found between ages of 30 and 50 years, although the study includes two children, ages 8 and 13. The chest was the most common site. Forty percent of the lesions were multinodular, and 23.3% showed ulceration. Histologic appearance is characterized in all cases by fusiform cells arranged like spokes around an empty hub. The fibroblastic origin was ascertained by electron-microscopic studies. The treatment used was broad surgical excision, removing tissue down to the aponeurosis to avoid recurrence.

Publication types

  • Comparative Study

MeSH terms

  • Adolescent
  • Adult
  • Age Factors
  • Aged
  • Child
  • Colombia
  • Female
  • Fibrosarcoma / diagnosis*
  • Fibrosarcoma / epidemiology
  • Fibrosarcoma / surgery
  • Humans
  • Male
  • Microscopy, Electron
  • Middle Aged
  • Sex Factors
  • Skin / pathology
  • Skin / ultrastructure
  • Skin Neoplasms / diagnosis*
  • Skin Neoplasms / epidemiology
  • Skin Neoplasms / surgery