Enhanced proteolytic degradation of normal beta-galactosidase in the lysosomal storage disease with combined beta-galactosidase and neuraminidase deficiency

Biochim Biophys Acta. 1982 Apr 21;703(1):69-76. doi: 10.1016/0167-4838(82)90012-7.
No abstract available

MeSH terms

  • Animals
  • Cattle
  • Electrophoresis, Polyacrylamide Gel
  • Endocytosis
  • Fibroblasts / metabolism
  • G(M1) Ganglioside / metabolism
  • Galactosidases / metabolism*
  • Gangliosidoses / enzymology*
  • Haplorhini
  • Humans
  • Male
  • Neuraminidase / deficiency*
  • Testis / enzymology
  • Time Factors
  • beta-Galactosidase / metabolism*

Substances

  • G(M1) Ganglioside
  • Galactosidases
  • Neuraminidase
  • beta-Galactosidase