IL-3 increases marrow and peripheral erythroid precursors in chronic pure red cell aplasia presenting in childhood

Br J Haematol. 1995 Feb;89(2):413-6. doi: 10.1111/j.1365-2141.1995.tb03320.x.

Abstract

In most patients with Diamond-Blackfan anaemia (DBA) the addition of IL-3 to in vitro cultures increases the number of erythroid progenitors. However, a small proportion of patients show an erythroid response to in vivo administration of IL-3. We treated two adult patients with corticosteroid-refractory DBA, who had shown a clear in vitro erythroid response to IL-3, with increasing doses of IL-3 (from 2.5 to 10 micrograms/kg/d) by subcutaneous injections for 7 and 9 weeks. Monitoring of marrow and circulating progenitors showed a sustained elevation of BFU-E and CFU-E as well as an increase of other progenitors and CD34+ cells during therapy. However, this effect did not translate into a clear clinical response, although transfusion requirements decreased transiently in one patient. This report shows that a sustained elevation of erythroid progenitors induced by in vivo IL-3 administration may not translate into an increase of mature red cells production in DBA patients.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Bone Marrow / pathology
  • Dose-Response Relationship, Immunologic
  • Erythroid Precursor Cells / physiology
  • Erythropoietin / therapeutic use
  • Fanconi Anemia / blood
  • Fanconi Anemia / therapy*
  • Female
  • Hematopoietic Stem Cells / physiology
  • Humans
  • Interleukin-3 / therapeutic use*
  • Middle Aged
  • Red-Cell Aplasia, Pure / blood
  • Red-Cell Aplasia, Pure / therapy*

Substances

  • Interleukin-3
  • Erythropoietin