Improvement of mouse beta thalassaemia by hydroxyurea

Br J Haematol. 1993 Jul;84(3):492-6. doi: 10.1111/j.1365-2141.1993.tb03106.x.

Abstract

The present report provides evidence that hydroxyurea (HU) improves the beta thalassaemic phenotype in mice receiving 200 mg/kg/d for 30 d. The haematocrit rose from 29 +/- 3% at day 0 to 37 +/- 4% at day 30 (P < 0.05), despite myelosuppression and decreased reticulocyte counts. The beta minor/alpha ratio of globin chain synthesis increased from 0.78 at day 0 to 0.97 at day 30 (P < 0.001). Membrane defects improved: the proportion of bound alpha chains decreased, the proportion of spectrin and ankyrin increased and red cell deformability also increased.

MeSH terms

  • Animals
  • Blood Proteins / drug effects
  • Erythrocyte Deformability / drug effects
  • Erythrocyte Indices / drug effects
  • Globins / biosynthesis
  • Hematocrit
  • Hydroxyurea / therapeutic use*
  • Leukocyte Count / drug effects
  • Membrane Proteins / drug effects
  • Mice
  • Mice, Inbred DBA
  • beta-Thalassemia / blood
  • beta-Thalassemia / drug therapy*

Substances

  • Blood Proteins
  • Membrane Proteins
  • Globins
  • Hydroxyurea