Cardiac surgery with extracorporeal circulation in severe factor VII deficiency

Haemostasis. 1993;23(1):65-8. doi: 10.1159/000216855.

Abstract

We describe here successful open heart surgery with extracorporeal circulation and haemodilution in a child with severe congenital factor VII deficiency. Substitution therapy was realized with factor VII concentrate (SD proconvertin concentrate, Bio-Transfusion). This is the first report case of successful cardiac surgery in severe congenital factor VII deficiency.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Extracorporeal Circulation*
  • Factor VII / administration & dosage
  • Factor VII / analysis
  • Factor VII / genetics
  • Factor VII Deficiency*
  • Heart Septal Defects, Atrial / surgery*
  • Hemodilution
  • Humans
  • Male
  • Postoperative Care
  • Preoperative Care
  • Prothrombin Time

Substances

  • Factor VII