Prenatal diagnosis of 30 fetuses at risk for fragile X syndrome

Am J Med Genet. 1996 Jul 12;64(1):187-90. doi: 10.1002/(SICI)1096-8628(19960712)64:1<187::AID-AJMG33>3.0.CO;2-H.

Abstract

The results of 30 prenatal diagnoses for fragile X syndrome are reported. Amniotic fluid cells were examined in 1 case, fetal blood in 4, and chorionic villi samples in the others. Of the 5 fetuses analyzed by cytogenetic methods, 1 had showed 4% of fraXq27.3 expression sites and the pregnancy was terminated. For 1 diagnosis, linkage analysis was used: the female fetus turned out to be normal. In 24 fetuses, the direct analysis of the mutation by StB12.3 probe was performed: 6 female and 3 male fetuses were found to carry a full mutation and 1 female fetus was found to carry a premutation. In 3 cases, the diagnoses were verified on fetal blood samples. Several tissues of 2 aborted male fetuses were analyzed for the fragile X mutation. The results are reported and discussed.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Chorionic Villi Sampling
  • DNA Methylation
  • Female
  • Fragile X Syndrome / diagnosis*
  • Fragile X Syndrome / genetics
  • Genetic Carrier Screening
  • Humans
  • Male
  • Pregnancy
  • Prenatal Diagnosis*