Evidence against chronic antigen-specific T lymphocyte activation in myasthenia gravis

J Neurosci Res. 1996 Aug 15;45(4):492-9. doi: 10.1002/(SICI)1097-4547(19960815)45:4<492::AID-JNR20>3.0.CO;2-1.

Abstract

Myasthenia gravis (MG) is an antigen-specific autoimmune disease caused by antibodies against acetylcholine receptors (AChR) at the post-synaptic membrane of the neuromuscular junction. Clinical and immunological data imply the involvement of AChR-specific T lymphocytes as helper cells for autoantibody production. Direct data to support this hypothesis, however, remain sparse. In the present study, a large population of MG patients was studied for evidence of peripheral blood T cell activation by several assays. Assays based on non-specific measurements of T cell activation as well as assays of antigen-specific clonal expansion were utilized. Levels of soluble IL-2 receptor in serum were modestly elevated in some patients, suggesting T cell activation. However, peripheral blood cells did not show evidence of IL-2 receptor expression or enhanced reactivity to IL-2 in culture. Clonable T cells selected for hypoxanthine phosphoribosyl transferase (hprt) mutation, another non-antigen-specific marker for T cell activation, were not seen with increased frequency except in patients treated with purine analogs. Antigen-specific T cell activation was measured by proliferation assays using heterologous and autologous sources of AChR. Antigen-restimulated peripheral blood cell cultures were cloned by limiting dilution. The vast majority of patients failed to show convincing evidence of AChR specific T cell activation or clonal expansion; only 2 of 44 patients demonstrated clonable autologous AChR-specific T cells. An alternative hypothesis of T cell involvement in MG is proposed in which T cell activation is discontinuous and predominantly directed at antigens other than AChR.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Animals
  • Antibody Specificity
  • Chronic Disease
  • Clone Cells / chemistry
  • Clone Cells / immunology
  • Female
  • Flow Cytometry
  • Humans
  • Lymphocyte Activation / genetics
  • Lymphocyte Activation / immunology*
  • Male
  • Membrane Proteins / immunology
  • Middle Aged
  • Mutation / immunology
  • Myasthenia Gravis / immunology*
  • Protein Structure, Tertiary
  • Receptors, Cholinergic / chemistry
  • Receptors, Cholinergic / immunology
  • Receptors, Interleukin-2 / immunology
  • Receptors, Interleukin-2 / metabolism
  • Recombinant Proteins / immunology
  • Solubility
  • T-Lymphocytes / chemistry
  • T-Lymphocytes / cytology
  • T-Lymphocytes / immunology*
  • Torpedo

Substances

  • Membrane Proteins
  • Receptors, Cholinergic
  • Receptors, Interleukin-2
  • Recombinant Proteins