Regulation of Purkinje cell alignment by reelin as revealed with CR-50 antibody

J Neurosci. 1997 May 15;17(10):3599-609. doi: 10.1523/JNEUROSCI.17-10-03599.1997.

Abstract

Cerebellar Purkinje cells are generated in the ventricular zone, migrate outward, and finally form a monolayer in the cortex. In reeler mice, however, most Purkinje cells cluster abnormally in subcortical areas. Reelin, the candidate reeler gene product recognized by the CR-50 monoclonal antibody, is concentrated in a cortical zone along which Purkinje cells are aligned linearly, implying that it may regulate their alignment. We used an in vitro system and a transplantation approach to analyze the function of Reelin. Explant culture for 7 d of cerebella isolated from wild-type and reeler mice at embryonic day 13 (E13) reproduced in a phenotype-dependent manner the two distinct arrangement patterns (linear vs clustered) of Purkinje cells. Extensive CR-50 binding to wild-type explants converted the linear pattern into a reeler-like, clustered pattern. On the other hand, when reeler explants lacking Reelin were crowned with an artificial layer of Reelin+ granule cells, some Reelin molecules were distributed into a superficial zone of the reeler explants, and Purkinje cells formed a linear pattern along the Reelin-rich overlay. This "rescue" effect was also inhibited by CR-50. Hence, Reelin is involved in the Purkinje cell alignment, and the lack of this activity may explain the malformation in reeler cerebella. We further injected Reelin+ granule cells into the fourth ventricle of E12-13 mice. Extensive incorporation of the injected Reelin+ cells into the ventricular zone, but not of Reelin- cells, forced Purkinje cells of the host cerebella to form an aberrant layer, suggesting that premigratory Purkinje cells may already be responsive to Reelin or Reelin-related signals.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antibodies, Monoclonal
  • Antibody Specificity
  • Cell Adhesion Molecules, Neuronal / analysis*
  • Cell Adhesion Molecules, Neuronal / genetics*
  • Cell Movement / physiology*
  • Cells, Cultured / chemistry
  • Extracellular Matrix Proteins / analysis*
  • Extracellular Matrix Proteins / genetics*
  • Female
  • Fetus / cytology
  • Gene Expression Regulation, Developmental / physiology
  • Mice
  • Mice, Neurologic Mutants
  • Nerve Tissue Proteins / analysis
  • Nerve Tissue Proteins / physiology
  • Phenotype
  • Pregnancy
  • Purkinje Cells / chemistry*
  • Purkinje Cells / cytology
  • Purkinje Cells / transplantation
  • Reelin Protein
  • Serine Endopeptidases
  • Signal Transduction / physiology

Substances

  • Antibodies, Monoclonal
  • Cell Adhesion Molecules, Neuronal
  • Extracellular Matrix Proteins
  • Nerve Tissue Proteins
  • Reelin Protein
  • Reln protein, mouse
  • Serine Endopeptidases