Are "early" and "late" T-acute lymphoblastic leukemias different diseases? A single center study of 34 patients

Leuk Lymphoma. 1996 May;21(5-6):437-42. doi: 10.3109/10428199609093441.

Abstract

Clinical and biological parameters were retrospectively reviewed in 34 cases of T-lineage acute lymphoblastic leukemia (T-ALL), classified as "early" (20 cases) or "late" (14 cases) subgroups, according to the degree of blast cell differentiation, assessed by immunophenotyping. In "early" T-ALL, age, co-expression of "immature" (CD34 and HLA-Dr) or myeloid (My+) antigens, proliferative activity (as evaluated by Ki67 monoclonal antibody), and expression of the "multidrug-resistance" (MDR) phenotype (as determined by C-219 monoclonal antibody) were significantly higher, while WBC count and expression of CDl0 were significantly lower, than in "late" T-ALL. Furthermore, although no statistically significant difference was found between the two groups, "late" T-ALL more frequently displayed a greater extramedullary tumor mass ("lymphoma-like" syndrome), LI FAB morphology and a normal karyotype. A single patient, with "late" T-ALL, also showed positivity for TCR gamma/delta chains, specific monoclonal antibodies. On the whole, 30 patients (88.2%) achieved complete remission: 16(80%) were "early" and 14(100%) "late" T-ALL. No statistical difference was found between the two groups with respect to disease free survival (42% vs 54% at six years), whereas median overall survival was significantly shorter in "early" T-ALL (23 months vs median not yet reached at six years for "late" T-ALL, p < 0.05). We conclude that "early" and "late" T-ALL show clinical and biological differences, that could perhaps justify differential therapeutic approaches.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Biomarkers, Tumor / analysis
  • Cell Differentiation
  • Child
  • Child, Preschool
  • Chromosome Aberrations
  • Disease-Free Survival
  • Female
  • Humans
  • Immunophenotyping
  • Leukemia-Lymphoma, Adult T-Cell / classification*
  • Leukemia-Lymphoma, Adult T-Cell / drug therapy
  • Leukemia-Lymphoma, Adult T-Cell / genetics
  • Leukemia-Lymphoma, Adult T-Cell / mortality
  • Leukemia-Lymphoma, Adult T-Cell / pathology
  • Leukocyte Count
  • Life Tables
  • Male
  • Middle Aged
  • Neoplasm Proteins / analysis
  • Neoplastic Stem Cells / chemistry
  • Neoplastic Stem Cells / pathology*
  • Prognosis
  • Remission Induction
  • Retrospective Studies
  • Survival Rate

Substances

  • Biomarkers, Tumor
  • Neoplasm Proteins