Multiple bcl-2/Ig gene rearrangements in persistent polyclonal B-cell lymphocytosis

Br J Haematol. 1997 Jun;97(3):589-95. doi: 10.1046/j.1365-2141.1997.852725.x.

Abstract

Persistent polyclonal B-cell lymphocytosis is a benign lymphoproliferative disorder of unknown aetiology occurring exclusively in women, characterized by typical binucleated lymphocytes, polyclonal expansion of B cells and elevated serum IgM. Owing to the role of Bcl-2 oncogene in inhibition of apoptosis, we have investigated the presence of the bcl-2/Ig gene rearrangement. Bcl-2/Ig gene rearrangement was determined by polymerase chain reaction targeting the usual breakpoint regions of the t(14;18). Bcl-2/Ig gene rearrangement was identified in all six patients and, more importantly, multiple rearrangements were present in five patients. The frequency of the bcl-2/Ig gene rearrangement is estimated to be of one translocation in 1 x 10(2) to 1 x 10(3) peripheral blood mononuclear cells. We conclude that persistent polyclonal B-cell lymphocytosis is associated with bcl-2/Ig gene rearrangement. These findings are of clinical importance because these patients may be misdiagnosed as having a leukaemic expression of non-Hodgkin's lymphoma.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Chromosomes, Human, Pair 14
  • Chromosomes, Human, Pair 18
  • Female
  • Gene Rearrangement, B-Lymphocyte*
  • Genes, Immunoglobulin / genetics*
  • Genes, bcl-2 / genetics*
  • Humans
  • Lymphocytosis / genetics*
  • Middle Aged
  • Polymerase Chain Reaction
  • Translocation, Genetic