Independent and opposing roles for Btk and lyn in B and myeloid signaling pathways

J Exp Med. 1998 Sep 7;188(5):833-44. doi: 10.1084/jem.188.5.833.

Abstract

Transphosphorylation by Src family kinases is required for the activation of Bruton's tyrosine kinase (Btk). Differences in the phenotypes of Btk-/- and lyn-/- mice suggest that these kinases may also have independent or opposing functions. B cell development and function were examined in Btk-/-lyn-/- mice to better understand the functional interaction of Btk and Lyn in vivo. The antigen-independent phase of B lymphopoiesis was normal in Btk-/-lyn-/- mice. However, Btk-/-lyn-/- animals had a more severe immunodeficiency than Btk-/- mice. B cell numbers and response to T cell-dependent antigens were reduced. Btk and Lyn therefore play independent or partially redundant roles in the maintenance and function of peripheral B cells. Autoimmunity, hypersensitivity to B cell receptor (BCR) cross-linking, and splenomegaly caused by myeloerythroid hyperplasia were alleviated by Btk deficiency in lyn-/- mice. A transgene expressing Btk at approximately 25% of endogenous levels (Btklo) was crossed onto Btk-/- and Btk-/-lyn-/- backgrounds to demonstrate that Btk is limiting for BCR signaling in the presence but not in the absence of Lyn. These observations indicate that the net outcome of Lyn function in vivo is to inhibit Btk-dependent pathways in B and myeloid cells, and that Btklo mice are a useful sensitized system to identify regulatory components of Btk signaling pathways.

MeSH terms

  • Agammaglobulinaemia Tyrosine Kinase
  • Agammaglobulinemia / enzymology
  • Agammaglobulinemia / genetics
  • Agammaglobulinemia / pathology
  • Animals
  • Autoimmune Diseases / enzymology
  • Autoimmune Diseases / genetics
  • B-Lymphocytes / enzymology*
  • B-Lymphocytes / immunology
  • B-Lymphocytes / pathology
  • Hematopoiesis / genetics
  • Hematopoiesis / immunology
  • Hematopoietic Stem Cells / enzymology*
  • Hematopoietic Stem Cells / immunology
  • Immunoglobulin Isotypes / biosynthesis
  • Immunoglobulin Isotypes / blood
  • Immunoglobulins / biosynthesis
  • Immunoglobulins / blood
  • Lymphocyte Count
  • Lymphopenia / enzymology
  • Lymphopenia / genetics
  • Lymphopenia / immunology
  • Mice
  • Mice, Inbred BALB C
  • Mice, Inbred C57BL
  • Mice, Inbred Strains
  • Mice, Knockout
  • Protein-Tyrosine Kinases / deficiency
  • Protein-Tyrosine Kinases / genetics
  • Protein-Tyrosine Kinases / physiology*
  • Receptors, Antigen, B-Cell / antagonists & inhibitors
  • Receptors, Antigen, B-Cell / physiology
  • Signal Transduction / genetics
  • Signal Transduction / immunology*
  • src-Family Kinases / deficiency
  • src-Family Kinases / genetics
  • src-Family Kinases / physiology*

Substances

  • Immunoglobulin Isotypes
  • Immunoglobulins
  • Receptors, Antigen, B-Cell
  • Protein-Tyrosine Kinases
  • Agammaglobulinaemia Tyrosine Kinase
  • Btk protein, mouse
  • src-Family Kinases