Fearnley I - Search Results

1

Dysregulated mitophagy and mitochondrial organization in optic atrophy due to OPA1 mutations.

Liao C, Ashley N, Diot A, Morten K, Phadwal K, Williams A, Fearnley I, Rosser L, Lowndes J, Fratter C, Ferguson DJ, Vay L, Quaghebeur G, Moroni I, Bianchi S, Lamperti C, Downes SM, Sitarz KS, Flannery PJ, Carver J, Dombi E, East D, Laura M, Reilly MM, Mortiboys H, Prevo R, Campanella M, Daniels MJ, Zeviani M, Yu-Wai-Man P, Simon AK, Votruba M, Poulton J. Liao C, et al. Among authors: fearnley i. Neurology. 2017 Jan 10;88(2):131-142. doi: 10.1212/WNL.0000000000003491. Epub 2016 Dec 14. Neurology. 2017. PMID: 27974645 Free PMC article.

2

TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III.

Bottani E, Cerutti R, Harbour ME, Ravaglia S, Dogan SA, Giordano C, Fearnley IM, D'Amati G, Viscomi C, Fernandez-Vizarra E, Zeviani M. Bottani E, et al. Mol Cell. 2017 Jul 6;67(1):96-105.e4. doi: 10.1016/j.molcel.2017.06.001. Epub 2017 Jun 29. Mol Cell. 2017. PMID: 28673544 Free article.

3

MR-1S Interacts with PET100 and PET117 in Module-Based Assembly of Human Cytochrome c Oxidase.

Vidoni S, Harbour ME, Guerrero-Castillo S, Signes A, Ding S, Fearnley IM, Taylor RW, Tiranti V, Arnold S, Fernandez-Vizarra E, Zeviani M. Vidoni S, et al. Cell Rep. 2017 Feb 14;18(7):1727-1738. doi: 10.1016/j.celrep.2017.01.044. Cell Rep. 2017. PMID: 28199844 Free article.

4

Loss of COX4I1 Leads to Combined Respiratory Chain Deficiency and Impaired Mitochondrial Protein Synthesis.

Čunátová K, Reguera DP, Vrbacký M, Fernández-Vizarra E, Ding S, Fearnley IM, Zeviani M, Houštěk J, Mráček T, Pecina P. Čunátová K, et al. Among authors: fearnley im. Cells. 2021 Feb 10;10(2):369. doi: 10.3390/cells10020369. Cells. 2021. PMID: 33578848 Free PMC article.

5

NDUFS3 depletion permits complex I maturation and reveals TMEM126A/OPA7 as an assembly factor binding the ND4-module intermediate.

D'Angelo L, Astro E, De Luise M, Kurelac I, Umesh-Ganesh N, Ding S, Fearnley IM, Gasparre G, Zeviani M, Porcelli AM, Fernandez-Vizarra E, Iommarini L. D'Angelo L, et al. Among authors: fearnley im. Cell Rep. 2021 Apr 20;35(3):109002. doi: 10.1016/j.celrep.2021.109002. Cell Rep. 2021. PMID: 33882309 Free PMC article.

6

SILAC-based complexome profiling dissects the structural organization of the human respiratory supercomplexes in SCAFI^KO cells.

Fernández-Vizarra E, López-Calcerrada S, Formosa LE, Pérez-Pérez R, Ding S, Fearnley IM, Arenas J, Martín MA, Zeviani M, Ryan MT, Ugalde C. Fernández-Vizarra E, et al. Among authors: fearnley im. Biochim Biophys Acta Bioenerg. 2021 Jul 1;1862(7):148414. doi: 10.1016/j.bbabio.2021.148414. Epub 2021 Mar 13. Biochim Biophys Acta Bioenerg. 2021. PMID: 33727070 Free article.

7

Evolution of respiratory complex I: "supernumerary" subunits are present in the alpha-proteobacterial enzyme.

Yip CY, Harbour ME, Jayawardena K, Fearnley IM, Sazanov LA. Yip CY, et al. J Biol Chem. 2011 Feb 18;286(7):5023-33. doi: 10.1074/jbc.M110.194993. Epub 2010 Nov 29. J Biol Chem. 2011. PMID: 21115482 Free PMC article.

8

Assembly factors for the membrane arm of human complex I.

Andrews B, Carroll J, Ding S, Fearnley IM, Walker JE. Andrews B, et al. Proc Natl Acad Sci U S A. 2013 Nov 19;110(47):18934-9. doi: 10.1073/pnas.1319247110. Epub 2013 Nov 4. Proc Natl Acad Sci U S A. 2013. PMID: 24191001 Free PMC article.

9

Fasting, but Not Aging, Dramatically Alters the Redox Status of Cysteine Residues on Proteins in Drosophila melanogaster.

Menger KE, James AM, Cochemé HM, Harbour ME, Chouchani ET, Ding S, Fearnley IM, Partridge L, Murphy MP. Menger KE, et al. Cell Rep. 2015 Jun 30;11(12):1856-65. doi: 10.1016/j.celrep.2015.05.033. Epub 2015 Jun 18. Cell Rep. 2015. PMID: 26095360 Free PMC article.

10

NDUFAF5 Hydroxylates NDUFS7 at an Early Stage in the Assembly of Human Complex I.

Rhein VF, Carroll J, Ding S, Fearnley IM, Walker JE. Rhein VF, et al. J Biol Chem. 2016 Jul 8;291(28):14851-60. doi: 10.1074/jbc.M116.734970. Epub 2016 May 18. J Biol Chem. 2016. PMID: 27226634 Free PMC article.

Save citations to file

Email citations

Send citations to clipboard

Add to Collections

Add to My Bibliography

Create a file for external citation management software

Your saved search

Your RSS Feed

My Custom Filters

Publication date

Text availability

Article attribute

Article type

Article Language

Species

Sex

Age

Other

129 results

Search Page

Filters